Longterm Outcomes of Living Donor Liver Transplantation for Glycogen Storage Disease Type 1b
Seiichi Shimizu, Seisuke Sakamoto, Reiko Horikawa, Akinari Fukuda, Hajime Uchida, Masahiro Takeda, Yusuke Yanagi, Rie Irie, Takako Yoshioka, Mureo Kasahara – 6 October 2019 – Glycogen storage disease (GSD) type 1b (Online Mendelian Inheritance in Man [OMIM] 232220) is an autosomal recessive inborn error of carbohydrate metabolism caused by defects in glucose‐6‐phosphate translocase. GSD1b patients have severe hypoglycemia with several clinical manifestations of hepatomegaly, obesity, a doll‐like face, and neutropenia.